Langerhans Cell Histiocytosis is a rare disease featuring aberrant proliferation of dendritic cells that can infiltrate the bony skeleton.The authors report a case of six-year-old female presenting with torticollis.She Footwear was found to have extensive lytic LCH lesions in the cranio-cervical junction, causing atlanto-axial rotatory subluxation.
Decision was made for a non-surgical approach to treat the patient.She was placed Lip Treatments in a Halo brace, and given concomitant chemotherapy.Post-treatment imaging demonstrated near-complete reconstitution of the skeleton affected by LCH.
This case highlights the feasibility of non-surgical treatment in selected LCH patients at high-risk of spinal instability.Keywords: Atlanto-axial subluxation, Langerhans cell histocytosis, Torticollis.